Objective: We report a recent case of epicardial cyst with constrictive pericarditis. Case report: A male patient aged 20 years presented with the complaint of swelling in both legs for one year. Magnetic resonance imaging of the heart revealed a cystic mass inside the pericardium adjacent to the right ventricle. The patient was operated on by cardiovascular surgeons, with the diagnosis of constrictive pericarditis, and a pericardiectomy was carried out. Discussion: Cardiac cysts originating from the epicardium in the pericardial cavity are extremely rare, with only a few cases reported up to now. We report here on an epicardial cyst occurring coincidentally with constrictive pericarditis for the first time in the literature.